Moderatively Severe Congenital Heart Disease

Moderately severe and complex congenital heart diseases include more serious defects that occur during the heart’s development. These conditions generally require surgical repair and long-term management at an ACHD center such as EACH. These patients should be seen periodically at adult congenital heart disease centers.

These conditions include:

  • Aorto-left ventricular fistulae
  • Anomalous pulmonary venous drainage (partial or total)
  • Atrioventricular canal defects (partial or complete)
  • Coarctation of the aorta
  • Ebstein’s anomaly
  • Infundibular right ventricular outflow obstruction of significance
  • Ostium primum atrial septal defect
  • Patent ductus arteriosus (not closed)
  • Pulmonary valve regurgitation (moderate to severe)
  • Pulmonic valve stenosis (moderate to severe)
  • Sinus of Valsalva fistula/aneurysm
  • Sinus venosus atrial septal defect
  • Subvalvar or supravalvar aortic stenosis (except HOCM†)
  • Tetralogy of Fallot
  • Ventricular septal defect with:
    • Absent valve or valves
    • Aortic regurgitation
    • Coarctation of the aorta
    • Mitral disease
    • Right ventricular outflow tract obstruction
    • Straddling tricuspid/mitral valve
    • Subaortic stenosis

†HOCM = hypertrophic obstructive cardiomyopathy