Moderately severe and complex congenital heart diseases include more serious defects that occur during the heart’s development. These conditions generally require surgical repair and long-term management at an ACHD center such as EACH. These patients should be seen periodically at adult congenital heart disease centers.
These conditions include:
- Aorto-left ventricular fistulae
- Anomalous pulmonary venous drainage (partial or total)
- Atrioventricular canal defects (partial or complete)
- Coarctation of the aorta
- Ebstein’s anomaly
- Infundibular right ventricular outflow obstruction of significance
- Ostium primum atrial septal defect
- Patent ductus arteriosus (not closed)
- Pulmonary valve regurgitation (moderate to severe)
- Pulmonic valve stenosis (moderate to severe)
- Sinus of Valsalva fistula/aneurysm
- Sinus venosus atrial septal defect
- Subvalvar or supravalvar aortic stenosis (except HOCM†)
- Tetralogy of Fallot
- Ventricular septal defect with:
- Absent valve or valves
- Aortic regurgitation
- Coarctation of the aorta
- Mitral disease
- Right ventricular outflow tract obstruction
- Straddling tricuspid/mitral valve
- Subaortic stenosis
†HOCM = hypertrophic obstructive cardiomyopathy
